Sinus venosus atrial septal defect (SV-ASD) can be a challenging diagnostic problem. It can present with non-specific signs and symptoms and, on imaging, can mimic other causes of right heart dilatation. Transthoracic echocardiography using standard scan planes may be limited, due to the defect and any associated anomalous pulmonary venous drainage lying outside the confines of the fossa ovalis. At our institution, we use cardiovascular magnetic resonance imaging (CMRI) as a problem-solving tool in these patients. In this article, we discuss the utility of CMRI in establishing the diagnosis by presenting our recent experience and illustrating it with sample cases. We wish to highlight the problems relating to making a diagnosis of SV-ASD in adult patients, and how CMRI has contributed to overcoming these in our practice.
To read this article in full you will need to make a payment
Purchase one-time access:Academic & Personal: 24 hour online accessCorporate R&D Professionals: 24 hour online access
One-time access price info
- For academic or personal research use, select 'Academic and Personal'
- For corporate R&D use, select 'Corporate R&D Professionals'
Subscribe:Subscribe to Heart, Lung and Circulation
Already a print subscriber? Claim online access
Already an online subscriber? Sign in
Register: Create an account
Institutional Access: Sign in to ScienceDirect
- Atrial septal defects in the adult: recent progress and overview.Circulation. 2006; 114: 1645-1653
- Sinus venosus atrial septal defect.Am Heart J. 1973; 85: 177-185
- Sinus venosus syndrome: atrial septal defect or anomalous venous connection? A multiplane transoesophageal approach.Heart. 2002; 88: 634-638
- Repair of congenital heart disease: a primer-part 1.Radiology. 2008; 247: 617-631
- Incidence of secondary pulmonary hypertension in adults with atrial septal or sinus venosus defects.Heart. 1999; 82 (30–33.5)
- Congenital heart disease in adults- first of two parts.N Engl J Med. 2000; 342: 256-263
- Long-term outcome after surgical repair of isolated atrial septal defect: follow-up at 27 to 32 years.N Engl J Med. 1990; 323: 1645-1650
- Diagnosis of sinus venosus atrial septal defect with transesophageal echocardiography.Circulation. 1996; 94: 1049-1055
- Ultrafast three-dimensional contrast enhanced magnetic resonance angiography and imaging in the diagnosis of partial anomalous pulmonary venous drainage.J Am Coll Cardiol. 2001; 37: 1120-1128
- Cardiac magnetic resonance imaging evaluation of sinus venosus defects: comparison to surgical findings.Pediatr Cardiol. 2007; 28: 51-56
- Computed tomography of partial anomalous pulmonary venous connection in adults.J Comput Assist Tomogr. 2003; 27: 743-749
- Dynamic contrast-enhanced MRI before and after transcatheter occlusion of patent foramen ovale.AJR Am J Roentgenol. 2007; 188: 844-849
- Clinical indications for cardiovascular magnetic resonance (CMR): consensus panel report.J Cardiovasc Magn Reson. 2004; 6: 727-765
- Left-to-right cardiac shunts: comparison of measurements obtained with MR velocity mapping and with radionuclide angiography.Radiology. 1999; 211: 453-458
- Cardiac MRI and pulmonary MR angiography of sinus venosus defect and partial anomalous pulmonary venous connection in cause of right undiagnosed ventricular enlargement.AJR Am J Roentgenol. 2009; 192: 259-266
Accepted: June 7, 2010
Received in revised form: May 27, 2010
Received: April 21, 2010
© 2010 Australasian Society of Cardiac and Thoracic Surgeons and the Cardiac Society of Australia and New Zealand. Published by Elsevier Inc. All rights reserved.