Sinus venosus atrial septal defect (SV-ASD) can be a challenging diagnostic problem.
It can present with non-specific signs and symptoms and, on imaging, can mimic other
causes of right heart dilatation. Transthoracic echocardiography using standard scan
planes may be limited, due to the defect and any associated anomalous pulmonary venous
drainage lying outside the confines of the fossa ovalis. At our institution, we use
cardiovascular magnetic resonance imaging (CMRI) as a problem-solving tool in these
patients. In this article, we discuss the utility of CMRI in establishing the diagnosis
by presenting our recent experience and illustrating it with sample cases. We wish
to highlight the problems relating to making a diagnosis of SV-ASD in adult patients,
and how CMRI has contributed to overcoming these in our practice.
Keywords
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Article info
Publication history
Accepted:
June 7,
2010
Received in revised form:
May 27,
2010
Received:
April 21,
2010
Identification
Copyright
© 2010 Australasian Society of Cardiac and Thoracic Surgeons and the Cardiac Society of Australia and New Zealand. Published by Elsevier Inc. All rights reserved.