Arrhythmogenic right ventricular cardiomyopathy (ARVC) is a disease affecting the
right, and/or the left ventricle, and commonly presents as an electrical disorder
with ventricular arrhythmias and increased risk of sudden cardiac death.
Abbreviations:
ARVC (arrythmogenic right ventricular cardiomyopathy), RV (right ventricle), LV (left ventricle), VA (ventricular arrhythmias), VT (ventricular tachycardia), TAPSE (tricuspid annular plane systolic excursion), EACVI (European Association of Cardiovascular Imaging), TFC (Task Force Criteria), CMR (cardiovascular magnetic resonance), CT (computed tomography), ICD (implantable cardioverter-defibrillator)Keywords
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References
- Arrhythmogenic right ventricular cardiomyopathy. Dysplasia, dystrophy, or myocarditis?.Circulation. 1996; 94: 983-991
- The mystery of arrhythmogenic right ventricular dysplasia/cardiomyopathy: from observation to mechanistic explanation.Circulation. 2006; 114: 1794-1795
- Comprehensive multi-modality imaging approach in arrhythmogenic cardiomyopathy-an expert consensus document of the European Association of Cardiovascular Imaging.Eur Heart J Cardiovasc Imaging. 2017; 18: 237-253
- Diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia: proposed modification of the Task Force Criteria.Eur Heart J. 2010; 31: 806-814
- Cardiac phenotype and long-term prognosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia patients with late presentation.. Heart Rhythm. 2017; 14: 883-891
- Incremental value of cardiac magnetic resonance imaging in arrhythmic risk stratification of arrhythmogenic right ventricular dysplasia/cardiomyopathy-associated desmosomal mutation carriers.J Am Coll Cardiol. 2013; 62: 1761-1769
- Exercise increases age-related penetrance and arrhythmic risk in arrhythmogenic right ventricular dysplasia/cardiomyopathy-associated desmosomal mutation carriers.J Am Coll Cardiol. 2013; 62: 1290-1297
- Systematic review: Impact of the new task force criteria in the diagnosis of arrhythmogenic right ventricular cardiomyopathy.Int J Cardiol. 2017; 241: 311-317
- Noninvasive diagnosis of electroanatomic abnormalities in arrhythmogenic right ventricular cardiomyopathy.Circ Arrhythm Electrophysiol. 2010; 3: 632-638
- Arrhythmogenic response to isoproterenol testing vs. exercise testing in arrhythmogenic right ventricular cardiomyopathy patients.Europace. 2018; 20: f30-f36https://doi.org/10.1093/europace/euy007
- 12-lead electrocardiogram to localize region of abnormal electroanatomic substrate in arrhythmogenic right ventricular cardiomyopathy.JACC Clin Electrophysiol. 2017; 3: 654-665
- High interobserver variability in the assessment of epsilon waves: implications for diagnosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia.Heart Rhythm. 2016; 13: 208-216
- Prolonged RV endocardial activation duration: a novel marker of arrhythmogenic right ventricular dysplasia/cardiomyopathy.Heart Rhythm. 2009; 6: 769-775
- The diagnostic performance of imaging methods in ARVC using the 2010 Task Force criteria.Eur Heart J Cardiovasc Imaging. 2014; 15: 1219-1225
- Right ventricular mechanical dispersion is related to malignant arrhythmias: a study of patients with arrhythmogenic right ventricular cardiomyopathy and subclinical right ventricular dysfunction.Eur Heart J. 2011; 32: 1089-1096
- Age-, body size-, and sex-specific reference values for right ventricular volumes and ejection fraction by three-dimensional echocardiography: a multicenter echocardiographic study in 507 healthy volunteers.Circ Cardiovasc Imaging. 2013; 6: 700-710
- Left ventricular involvement in arrhythmogenic right ventricular dysplasia/cardiomyopathy assessed by echocardiography predicts adverse clinical outcome.J Am Soc Echocardiogr. 2015; 28: 1103-1113 e9
- CMR features of ARVC/D.in: Marcus F.I. Cardiac MRI in diagnosis, clinical management, and prognosis of arrhythmogenic right ventricular cardiomyopathy/dysplasia. Academic Press, 2016
- Genetic evaluation of cardiomyopathy—a heart failure society of america practice guideline.J Card Fail. 2018; 24: 281-302
- Risk stratification in arrhythmogenic right ventricular cardiomyopathy.Circulation. 2017; 136: 2068-2082
- Annual rate of transvenous defibrillation lead defects in implantable cardioverter-defibrillators over a period of >10 years.Circulation. 2007; 115: 2474-2480
- Long-term right ventricular implantable cardioverter-defibrillator lead performance in arrhythmogenic right ventricular cardiomyopathy.Heart Rhythm. 2016; 13: 1964-1970
- Mobile thrombus on device leads in patients undergoing ablation: identification, incidence, location, and association with increased pulmonary artery systolic pressure.Circulation. 2011; 124: 772-778
- Imaging of scar in patients with ventricular arrhythmias of right ventricular origin: cardiac magnetic resonance versus electroanatomic mapping.J Cardiovasc Electrophysiol. 2011; 22: 1359-1366
- Long-term outcome with catheter ablation of ventricular tachycardia in patients with arrhythmogenic right ventricular cardiomyopathy.Circ Arrhythm Electrophysiol. 2015; 8: 1413-1421
- Right ventricular morphology on catheter angiography: variations and its implications for the diagnosis of arrhythmogenic right ventricular cardiomyopathy.Heart Lung Circ. 2012; 21: 700-705https://doi.org/10.1016/j.hlc.2012.06.002
Article info
Publication history
Published online: April 18, 2019
Received:
January 31,
2019
Identification
Copyright
Crown Copyright © 2019 Published by Elsevier B.V. on behalf of Australian and New Zealand Society of Cardiac and Thoracic Surgeons (ANZSCTS) and the Cardiac Society of Australia and New Zealand (CSANZ). All rights reserved.